Behavior Issues

I've always heard that behavior is a problem for CHARGE kids and I guess I sort of pushed it to the back of my mind. I figured there was no need to worry until we had to deal with it. Unfortunately, we are now dealing with it. Ben has started to hit his head on the ground when angry and hit himself in the face. It is so difficult to deal with and we are struggling with ways to stop it. By responding, we seem to be reinforcing the behavior. By not responding, I'm worried he is going to hurt himself since his threshold for pain is so high. We are reading a book that is suppose to shed some light on why the behavior happens and I'm so hoping it will offer techniques that will help.